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• Conditions (26): Achalasia, Genetic and Rare Conditions, Darier's Disease, and 23 others Achalasia, Genetic and Rare Conditions, Darier's Disease, Inflammatory Linear Verrucous Epidermal Nevus, Behcet's Syndrome, Lichen Planus, Menkes Kinky Hair Syndrome, Epidermal Nevus, Hailey-Hailey disease, Marfan syndrome, Kartagener Syndrome, Friedreich's Ataxia, Angelman syndrome, Elephantiasis, Keratosis Follicularis Squamosa, Agenesis of Corpus Callosum, Hirschsprung's Disease, Trimethylaminuria, Albinism, Addison's Disease, Anencephaly, Ehlers-Danlos syndrome, Dercum's Disease, Fragile X Syndrome, Dandy Walker Syndrome, dermatitis [hide]
• Groups (37): Scleroderma, Achalasia, Beckers Nevus, and 34 others Scleroderma, Achalasia, Beckers Nevus, Darier's Disease, Lichen Sclerosis, Lichen Planus, Hidradenitis Suppurativa, Granuloma Annulare, Sweet Syndrome, Alopecia Areata, Rare 'Orphan' Disorders, Hirschsprung's Disease, PANDAS Syndrome, Trimethylaminuria, Agenesis of Corpus Callosum, Dercum's Disease, Addison's Disease, Blepharophimosis, Anencephaly, Dandy Walker Syndrome, Fragile X Syndrome, Pachygyria, Ledderhose Disease, Aarskog Syndrome, Legg-Calve-Perthes Disease, Microphthalmia, Cri-du-Chat Syndrome, Behcet's Syndrome, Empty Sella Syndrome, Cleidocranial Dysplasia, 1p36 Deletion Syndrome, Fructose Intolerance, Kartagener Syndrome, Cushing's Syndrome, Menkes Kinky Hair Syndrome, Short Bowel Syndrome, Androgen Insensitivity Syndrome [hide]
• Symptoms (21): Scleroderma, Von Willebrand disease, Blepharophimosis, and 18 others Scleroderma, Von Willebrand disease, Blepharophimosis, Sweet Syndrome, Club Foot, Castleman's Disease, Granuloma Annulare, Alopecia Areata, Raynaud's Disease and Phenomenon, pyoderma gangrenosum, Tetralogy of Fallot, Angioedema, Achalasia, red skin rash, Mole, Skin Findings, Port-Wine Stain, Urticaria, Symptoms and Side Effects, Sclerodactyly, Erythema [hide]
• Treatments (26): Heller's myotomy for achalasia, Pneumatic dilatation for achalasia, Relaxation of scar or web contracture of skin, and 23 others Heller's myotomy for achalasia, Pneumatic dilatation for achalasia, Relaxation of scar or web contracture of skin, Esophageal Dilatation, hydroquinone 40 MG/ML Topical Cream, Benzatropine Methanesulfonate, Tolazoline Hydrochloride, Tolazoline, Heller Myotomy, achondroplasia, Dermabrasion, Trihexyphenidyl Hydrochloride, Alendronate 35 MG Oral Tablet, HYDROQUINONE 4 %, Benztropine 1 MG Oral Tablet, Alendronate 35 MG, Benztropine 1 MG/ML Injectable Solution, Alendronate 5 MG Oral Tablet, Alendronate, Trihexyphenidyl 2 MG Oral Tablet, dioxybenzone 30 MG/ML / ETHYL DIHYDROXYPROPYL PABA 50 MG/ML / hydroquinone 40 MG/ML Topical Cream, Other OR therapeutic procedures on skin and breast, hydroquinone 40 MG/ML / padimate-O 30 MG/ML Topical Cream, dioxybenzone 0.03 MG/MG / ETHYL DIHYDROXYPROPYL PABA 0.05 MG/MG / hydroquinone 0.04 MG/MG Topical Gel, risedronate sodium, POTASSIUM PARA-AMINOBENZOATE 100 GM [hide]

About CREST Syndrome

The limited form of scleroderma is much milder: it has a slow onset and progression, skin hardening is usually confined to the hands and face, internal organ involvement is less severe, and a much better prognosis is expected. In typical cases of limited scleroderma, Raynaud's phenomenon may precede... more

The limited form of scleroderma is much milder: it has a slow onset and progression, skin hardening is usually confined to the hands and face, internal organ involvement is less severe, and a much better prognosis is expected.
In typical cases of limited scleroderma, Raynaud's phenomenon may precede scleroderma by several years. Raynaud's phenomenon is due to vasoconstriction of the small arteries of exposed peripheries - particularly the hands and feet - in the cold. It is classically characterised by a triphasic colour change - first white, then blue and finally red on rewarming. The scleroderma may be limited to the fingers - known as sclerodactyly.

The limited form is often referred to as CREST syndrome. "CREST" is an acronym for:
Calcinosis
Raynaud's syndrome
Esophageal dysmotility (See Achalasia)
Sclerodactyly
Telangiectasia
These are the five major signs that make up the CREST syndrome.

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