Related Content

• Conditions (26): Achalasia, Genetic and Rare Conditions, Darier's Disease, and 23 others Achalasia, Genetic and Rare Conditions, Darier's Disease, Lichen Planus, Inflammatory Linear Verrucous Epidermal Nevus, Behcet's Syndrome, Menkes Kinky Hair Syndrome, Marfan syndrome, Epidermal Nevus, Kartagener Syndrome, Hailey-Hailey disease, Friedreich's Ataxia, Agenesis of Corpus Callosum, Hirschsprung's Disease, Trimethylaminuria, Angelman syndrome, Addison's Disease, Elephantiasis, Anencephaly, Keratosis Follicularis Squamosa, Dercum's Disease, Fragile X Syndrome, Dandy Walker Syndrome, dermatitis, Cystic Fibrosis, 1p36 Deletion Syndrome [hide]
• Groups (37): Scleroderma, Achalasia, Beckers Nevus, and 34 others Scleroderma, Achalasia, Beckers Nevus, Darier's Disease, Lichen Sclerosis, Lichen Planus, Hidradenitis Suppurativa, Sweet Syndrome, Granuloma Annulare, Alopecia Areata, Rare 'Orphan' Disorders, Hirschsprung's Disease, PANDAS Syndrome, Agenesis of Corpus Callosum, Trimethylaminuria, Dercum's Disease, Addison's Disease, Blepharophimosis, Anencephaly, Dandy Walker Syndrome, Fragile X Syndrome, Pachygyria, Ledderhose Disease, Aarskog Syndrome, Legg-Calve-Perthes Disease, Microphthalmia, Cri-du-Chat Syndrome, Behcet's Syndrome, Cleidocranial Dysplasia, Fructose Intolerance, 1p36 Deletion Syndrome, Kartagener Syndrome, Empty Sella Syndrome, Menkes Kinky Hair Syndrome, Cushing's Syndrome, Androgen Insensitivity Syndrome, Esophageal Atresia and/or Tracheosophageal Fistula [hide]
• Symptoms (21): Blepharophimosis, Scleroderma, Von Willebrand disease, and 18 others Blepharophimosis, Scleroderma, Von Willebrand disease, Sweet Syndrome, Club Foot, Granuloma Annulare, Castleman's Disease, Alopecia Areata, Raynaud's Disease and Phenomenon, Achalasia, Angioedema, pyoderma gangrenosum, Tetralogy of Fallot, red skin rash, Skin Findings, Urticaria, Mole, Port-Wine Stain, Sclerodactyly, Symptoms and Side Effects, Erythema [hide]
• Treatments (26): Heller's myotomy for achalasia, Pneumatic dilatation for achalasia, Relaxation of scar or web contracture of skin, and 23 others Heller's myotomy for achalasia, Pneumatic dilatation for achalasia, Relaxation of scar or web contracture of skin, Esophageal Dilatation, Tolazoline Hydrochloride, Tolazoline, hydroquinone 40 MG/ML Topical Cream, Dermabrasion, Benzatropine Methanesulfonate, Potassium aminobenzoate, Chloroquine 50 MG/ML Injectable Solution, 4-Aminobenzoic Acid 10 MG/ML Oral Solution, CHLOROQUINE HYDROCHLORIDE 50 MG/ML, CHLOROQUINE PHOSPHATE 500 MG, POTASSIUM PARA-AMINOBENZOATE 2 GM, chloroquine diphosphate, Chloroquine hydrochloride, 4-Aminobenzoic Acid 300 MG / Salicylic Acid 300 MG Enteric Coated Tablet, Potassium aminobenzoate 100000 MG Oral Solution, POTASSIUM PARA-AMINOBENZOATE 100 GM, EPOPROSTENOL SODIUM 1.5 MG, Epoprostenol Sodium, Epoprostenol, Chloroquine, Chloroquine 250 MG Oral Tablet, 4-Aminobenzoate 500 MG Oral Capsule [hide]

About CREST Syndrome

The limited form of scleroderma is much milder: it has a slow onset and progression, skin hardening is usually confined to the hands and face, internal organ involvement is less severe, and a much better prognosis is expected. In typical cases of limited scleroderma, Raynaud's phenomenon may precede... more

The limited form of scleroderma is much milder: it has a slow onset and progression, skin hardening is usually confined to the hands and face, internal organ involvement is less severe, and a much better prognosis is expected.
In typical cases of limited scleroderma, Raynaud's phenomenon may precede scleroderma by several years. Raynaud's phenomenon is due to vasoconstriction of the small arteries of exposed peripheries - particularly the hands and feet - in the cold. It is classically characterised by a triphasic colour change - first white, then blue and finally red on rewarming. The scleroderma may be limited to the fingers - known as sclerodactyly.

The limited form is often referred to as CREST syndrome. "CREST" is an acronym for:
Calcinosis
Raynaud's syndrome
Esophageal dysmotility (See Achalasia)
Sclerodactyly
Telangiectasia
These are the five major signs that make up the CREST syndrome.

less